Liver involvement in patients with Gaucher disease types I and III

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Pulmonary involvement in Gaucher disease

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Fibroblasts from normal subjects and patients with the three types of Gaucher disease were labeled with [3H]leucine. Glucocerebrosidase antigen was immunoprecipitated using affinity-purified Sepharose-bound antibody. Normal cells initially formed a 60-kDa polypeptide antigen that was gradually replaced by a broad band of antigen averaging 63 kDa. This position corresponds with that of mature fi...

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ژورنال

عنوان ژورنال: Molecular Genetics and Metabolism Reports

سال: 2020

ISSN: 2214-4269

DOI: 10.1016/j.ymgmr.2019.100564